Cystic fibrosis (CF) is a condition passed down through families that causes a buildup of thick and sticky mucus in the lungs, digestive tract, and other areas of the body. It is one of the most common chronic lung diseases in children and young adults. It affects about 30,000 people in the United States and approximately 70,000 worldwide.
Cystic Fibrosis is caused by a defective gene that causes the body to produce abnormally thick and sticky fluid, called mucus. This mucus builds up in the breathing passages of the lungs and in the pancreas, the organ that helps to break down and absorb food. This collection of sticky mucus results in lung infections and serious digestion problems. The disease may also affect the sweat glands and the male reproductive system.
Millions of Americans carry the defective Cystic Fibrosis gene, but do not have any symptoms. That’s because a person with Cystic Fibrosis must inherit two defective Cystic Fibrosis genes—one from each parent. Most children with CF are diagnosed by age 2. A small number, however, are not diagnosed until age 18 or older. These patients usually have a milder form of the disease.
A blood test is available to help detect Cystic Fibrosis. The test looks for variations in a gene known to cause the disease.
Thanks to advances in therapies and patient care, more people with cystic fibrosis are surviving into their adult years than ever before. To help enhance the quality of life when treating Cystic Fibrosis, patients, families and caregivers can expect to maintain a close and collaborative care relationship with their healthcare team to determine and understand treatment options at every stage of the condition; learn and practice ways to stay healthy and limit exposure to germs; create and abide by a consistent treatment routine; and manage diet and exercise, among other activities.
An early diagnosis of Cystic Fibrosis and a comprehensive treatment plan can improve both survival rates and quality of life. Follow-up and monitoring are very important. If possible, patients should be cared for at Cystic Fibrosis specialty clinics that focus specifically on the diagnosis, treatment and support of the condition. When children reach adulthood, they should transfer to a Cystic Fibrosis specialty center for adults.
Lung problems are also treated with aerobic exercise or other therapies to thin the mucus and make it easier to cough up out of the lungs.
Kroger Specialty Pharmacy's total life care programs set a clear path to caring, compassionate Cystic Fibrosis therapy management and support.
We are here to provide patients, providers and partners with the necessary coordination of care vital to achieving successful treatment outcomes. By utilizing our expert patient care team comprised of Doctors of Pharmacy, registered pharmacists and nurses, reimbursement specialists and dedicated Patient Care Coordinators (PCCs), we are able to offer each and every patient and partner with high-quality, personalized care, ongoing patient evaluation and clinical support including frequent patient follow-up and continual education about their Cystic Fibrosis treatment.